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Williams–Campbell syndrome (WCS) is a disease of the airways where cartilage in the bronchi is defective. It is a form of congenital cystic bronchiectasis. This leads to collapse of the airways and bronchiectasis. It acts as one of the differential to allergic bronchopulmonary aspergillosis.
2 days ago · Williams-Campbell syndrome (WCS) is a rare form of congenital cystic bronchiectasis, in which distal bronchial cartilage is defective. Clinical presentation. Williams-Campbell syndrome may present with recurrent pneumonia, wheezing, pulmonary hypertension, barrel-chest deformity, and Harrison sulcus 8,10. Pathology.
Williams-Campbell Syndrome (WCS) is a rare congenital syndrome characterized by defective or completely absent bronchial wall cartilage in subsegmental bronchi, leading to distal airway collapse, producing a mechanical abnormality that may contribute to the formation of bronchiectasis distal to the collapsed bronchi.
Nov 2, 2021 · Williams-Campbell syndrome is a rare disease characterized by deficiency of cartilage typically in the fourth- to sixth-order bronchi, or sometimes in the mainstem bronchi, which results in cystic bronchiectasis and expiratory airway collapse ( 1 ).
INTRODUCTION: Williams-Campbell syndrome (WCS), also known as bronchomalacia, is a rare form of bronchiectasis that develops due to markedly diminished or absent cartilage around the sub-segmental bronchi, resulting in dilation of the subsequent bronchi.
Apr 15, 2024 · Williams-Campbell syndrome (WCS) is a congenital disorder which was first described in 1960 by Howard Williams and Peter Campbell among five children with respiratory manifestations due to cartilage deficiency of the bronchial walls (Williams and Campbell 1960).
A rare, respiratory malformation characterized by defective or completely absent bronchial wall cartilage in subsegmental bronchi, leading to distal airway collapse and contributing to the formation of bronchiectasis. The defect is mostly present between the fourth and sixth order bronchial divisions.
